I-Dystrophy ezinganeni

Umbuzo wokudla okunempilo kanye nesimiso somzimba emzimbeni wengane uthatha, ngokungangabazeki, bonke abazali. Kulesi sihloko, sizoxoxa ngesinye sezimo zokudangala kokudla - ukushaywa indiva, futhi ucabangele izimbangela nezimpawu zokuvela kwesinye sezifo ezibi kakhulu - i-congenital muscular dystrophy ezinganeni.

I-dystrophy yezingane

I-Dystrophy ivame ukubizwa ngokuthi enye yezinhlobo zokudabuka kokudla, okuholela ekunciphiseni kancane kancane kwazo zonke izinhlelo kanye nezitho zomzimba womuntu, okuholela ekutheni umzimba ungakwazi ukusebenza ngendlela evamile. Ngokuya ngobukhulu bokubonakaliswa, i-dystrophy ingaba mnene noma ikhulu (nakuba kunzima ukudweba umugqa ocacile phakathi kwalezi fomu). Ukuqina okukhulu kwe-dystrophy kubizwa ngokuthi i-atrophy.

Izimbangela ze-dystrophy

Phakathi kwezici ezandisa ingozi yokuthuthukisa i-dystrophy, ukuhlukanisa phakathi kwangaphakathi nangaphakathi. Ngaphandle kuhlanganisa imiphumela emibi yemvelo, ukunganeliseki noma ukungondleki ngokwanele, isimo esingokomzimba esingokomzimba. Ngokuvamile isizathu sokungondleki kungase singabi nobisi obanele obuvela kumama, ukuhoxiswa noma izinsipho eziphambene (okwenza kube nzima ukuncelisa), izigulane ezinomsoco eziqinile, ukuvilapha kwengane lapho usana. Ngokuvamile, umsebenzi wokuncelisa awunelisekile ebuthakathakeni, ezinganeni zakudala noma kulabo abaye baba ne-asphyxia noma ezinye izinkinga zokubeletha. Ngokuvamile imbangela yentuthuko yokudambisa umzimba ilahlekelwa yidlame ngenxa yokudla okungalungile, isingeniso esinzima sokudla okuhambisanayo, njll. Izifo ezihlukahlukene (zombili ezibelethwe futhi ezitholakalayo) zingaba nomthelela kulesi sifo se-metabolism.

I-Dystrophy: izimpawu

Isibonakaliso sokuqala sokudla komzimba kungukunciphisa uketshezi lwamafutha omzimba emzimbeni (kuqala ngesisu, bese kuthi esifubeni, izingalo nemilenze, futhi kamuva ebusweni). Isigaba sokuqala sesifo sibizwa ngokuthi i-hypotrophy. Odokotela bahlukanisa izigaba ezintathu zalo:

1. Ukungabi nesisindo akudluli ku-15% wendabuko. Ukukhula kuvamile, emzimbeni nasemilenzeni uhla lwe-fatty wehliswa kancane, umbala wesikhumba unamahlombe kancane, kodwa ngokuvamile awuhambanga ngaphezu komkhuba. Umsebenzi wezitho nezinhlelo zomzimba awuphukile.
2. Ukungabi nesisindo ebangeni elingama-20-30%, ukukhula ngaphansi kwesimiso ngo-1-3 cm, umzimba unciphisa uhlaka lwamafutha angaphansi kwesikhumba, imisipha iyinhlanhla, i-turgor of tiscues incishisiwe. Isikhumba siphume, siya emaphethweni. Uveze ukwephulwa kwesifiso, ukulala, isimo sengqondo asizinzile. Ukuthuthukiswa kwesistimu ye-musculoskeletal kuphazanyiswa.
3. Ukungabi nesisindo esingaphezu kuka-30% kuyisibonakaliso se-grade 3 hypotrophy. Ngesikhathi esifanayo, ukukhubazeka kokuthuthukiswa nokulinda ukukhula kuphawuleka kahle. Amafutha angaphansi kwenyama ayengekho, isikhumba sigcwele imibimbi, amehlo awela, isinkwa sisho. Kukhona ukubonakala kwamathambo okusobala, i-fontanel enkulu idonselwa kuyo. Ukudla kuphukile noma kungekho, isiguli sinomile, isifo sohudo. Ukuthuthukiswa kwezifo ezithathelwanayo kukhula, ngoba amandla omzimba ayisisekelo. Ngenxa yokuqina kwegazi, i-hemoglobin nenombolo yamaseli abomvu ayenyuka.

I-dystrophy ye-muscular progression iqoqo lezifo ezizuzwa njengezifo zomzimba womzimba. Abacwaningi bamanje basikisela ukuthi ukuthuthukiswa kwayo kuhlotshaniswa nokuphulwa komzimba we-enzyme, kodwa ayikho idatha eqondile kulokhu okwamanje. E-dystrophy yama-muscular, imisipha ikhula kancane (kaningi ngokungahambisani, njengama-asymmetrically), amandla e-muscle ancipha ngokulingana ngokulingana nesilinganiso sokuthuthukiswa komonakalo wesisindo. Uma umntwana eqala ukuguqula ubuso bakhe ngesikhathi sokukhulelwa (ukuma kwesikhumba, ukugoceka noma izinga lokuxhumana kwamehlo, ubukhulu bezindebe) - thintana nodokotela, kungase kube ukubonakaliswa kokuqala kokuthuthukiswa kwesifo sofuba emashumini asebasha.

Ukuze kutholakale ukuthi "i-dystrophy", udokotela kumele ahlole ingane, ahlole idatha ngokukhula, isisindo, ijubane kanye nemvelo yokuthuthukiswa kwezitho nezinhlelo zomzimba wengane.

Ukwelashwa kwesifo socansi ezinganeni

Ukwelashwa kwesifo sokudla komzimba kuyinkimbinkimbi, futhi kukhethwa ukucabangela iminyaka, isimo somntwana kanye nenani lomonakalo emzimbeni, kanye nesimo sesifo kanye nezimbangela zokuthuthukiswa kwayo.

Ingxenye ebaluleke kunazo zonke futhi ephoqelekile yokwelashwa ukuqokwa kokudla okufanele - iminyaka egcwele futhi efanelekile. Kukhonjisiwe futhi yi-vitamin therapy, i-vitamin supplementation ne-vitamin-mineral complexes. Uma kuphakama ubukhulu besifo, ukuqapha okukhulu ukuletha izinguquko ekudleni - ukwanda okukhulayo ekudleni kungabangela ukuwohloka ngisho nokufa kwesiguli. Yingakho inqubo yokwelapha kumele ibe ngaphansi kokuqondiswa odokotela.