I-cystic fibrosis ezinganeni

I-cystic fibrosis yisifo esibi kakhulu esithinta zonke izimo zomzimba womuntu ezikhiqiza i-mucus-ukuphefumula, ukugaya ukudla, isondo, ukugcoba. Lesi sifo sivame kakhulu, kodwa kuze kube yamuva, ukunaka kabanzi ukwelashwa kwakhe akukhanjwanga. Iziguli ze-Cystic fibrosis kufanele zithole imithi ekhethiwe kahle ngesikhathi sokuphila kwayo yonke, zihlolwa njalo futhi ziphathwe unomphela phakathi nezinkathi zokucima amandla.

Imbangela nezinhlobo ze-cystic fibrosis

Isizathu saleso sifo siyishintsho se-gene cystic fibrosis. Izakhi zatholakala kuphela eminyakeni engamashumi amathathu edlule. Ukuguqulwa kwalesi sifo kuholela ekutheni imfihlo efihliwe yizigulane iba kakhulu kakhulu. Imfihlo ejulile igxila emahlathini nasezikhungwini, ikhula ezincane ezincane eziphilayo - ngokuvamile i-Pseudomonas aeruginosa, i-Staphylococcus aureus, intonga ye-hemophilic. Ngenxa yalokho, ukuvuvukala okungapheli kuyaqala.

I-cystic fibrosis ivela ngezinhlobo ezintathu:

• i-pulmonary;
• emathunjini;
• kuxutshwe.

Izimpawu ze-cystic fibrosis ezinsana

1. Ukuvimbela emathunjini (i-mekonial ileus) - emathunjini amancane ukungena kwamanzi, i-sodium ne-chlorine iyaphazanyiswa, ngenxa yokuthi ihlanganiswe ne-meconium. Isibeletho sivuvukala emntwaneni, sibheka nge-bile, isikhumba soma futhi sibucayi, i-pattern ye-vascular ivela esiswini, ingane iba buthakathaka futhi ingasebenzi, izimpawu zokuzibulala zibonakala ngamathole
2. I-jaundice ehlala isikhathi eside - iboniswe engxenyeni yamacala e-ileus ye-meconial, kodwa futhi iyisibonakaliso esizimele sesifo. Kuvela ngoba i-bile iba kakhulu kakhulu futhi igeleza kahle ngaphandle kwe-gallbladder.
3. Ingane ibeka amakristalu kasawoti esikhunjeni sobuso kanye nezimpumputhe, isikhumba sibe ukunambitheka okusawoti.

Izimpawu ze-cystic fibrosis ezinganeni

Ngokuvamile, i-cystic fibrosis ibonakala lapho usana ludluliselwa ekudleni okuxubene noma olujojowe ngokudla okuhambisanayo:

1. Isihlalo siba mnandi, sinamafutha, siningi futhi siyamcasula.

2. Isibindi sanda.

3. Kungase kube khona iphutha le-rectum.

4. Ingane iyalandela ngemuva kokuthuthukiswa ngokomzimba futhi iveza izimpawu zokudonswa komzimba:

• isikhumba soma futhi siphelile;
• ikhula futhi ilulaze i-thorax;
• isisu sibe sikhulu futhi siguquke;
• Izingalo nemilenze ziba mncane ngeminwe ye-phalanxes "njengama-drumsticks."

5. Emntwaneni obeletha uqala ukukhwehlela okwomile okungapheli. I-mucus enamandla igxila ku-bronchi futhi iphazamise ukuphefumula okuvamile. Esikhathini esingaphansi kwamagciwane, amabhaktheriya aphindaphindiwe ngenkuthalo, ngenxa yokuthi kukhona ukuvuvukala okwegazi.

Izingane ezine-cystic fibrosis kufanele zithole ukwelashwa okufanele. Izinkimbinkimbi zokwelapha zihlanganisa:

• Ukwelashwa kwe-antibacterial - ukulwa nokutheleleka ohlelweni lokuphefumula;
• ukwelashwa kwe-mucolytic - ukwenzela ukuqubuka kwe-sputum;
• i-kinesitherapy - ukuzivocavoca okukhethekile;
• i-hepatoprotectors - yokukhipha i-bile;
• Ukwelashwa kwe-Vitamin - ukukhokhela ukulahlekelwa amavithamini nesitolishi.

Ukuhlolwa kwezinsana ze-cystic fibrosis

I-cystic fibrosis ingathathwa njengemiphumela yokuhlolwa kwemitholampilo kanye ne-laboratory yesiguli. Ukuze lesi sifo sitholakale ngokushesha ngangokunokwenzeka, i-cystic fibrosis ifakiwe ohlelweni lokuhlola izingane ezisanda kuzalwa ngenxa yezifo ezizalana nezifo.

Ukuhlolisisa ingane esesibhedlela kuyothatha isampula yegazi (ngokuvamile esivela esithendeni) ngendlela "eyomile eyomile". Lokhu kwenziwa ngosuku lwesine ezinganeni ezelwe ngesikhathi noma ngosuku lwama-7 ezinsana ezingakafiki. Isampula segazi sisetshenziselwa umugqa wokuhlola, okubekwa ngaphansi kwesifundo ku laboratory. Uma kukhona ukusola kwe-cystic fibrosis, abazali baziswa ngokuphuthumayo ngesidingo sokuhlolwa okwengeziwe.