Isifo se-Hirschsprung singumgogodla wokubeletha wezinambuzane ezinkulu. Isiguli asinayo amangqamuzana omzimba we-plexus of Meissner ne-plexus ye-Auerbach. Ngenxa yokungabi khona kwanoma yikuphi ukuphazamiseka endaweni ethintekile kanye nokwehla kwesinye isikhathi eminye iminyango, kunomkhawulo owandayo nokwandisa kwamanzi.
Izimpawu zesifo sikaHirschsprung
Izimpawu zokuqala zesifo sikaHirschsprung ziyi-flatulence, ukuqotshwa kanye nokwanda kwesikhumba esiswini. Uma isiguli singabonisi kudokotela, izimpawu eziseduze ziqala ukuvela. Lokhu kufaka:
- i-anemia ;
- i-hypotrophy;
- amatshe amaqabunga.
Kwezinye izimo, iziguli zizwa ubuhlungu esiswini, amandla abo angakhula njengoba isikhathi sokuqothulwa sisanda.
Izigaba zesifo seHirschsprung
I-syndrome yeHirschsprung iqala ngezigaba eziningana. Isigaba sokuqala saleso sifo sihlawulelwa: isiguli sinokuqothulwa, kodwa isikhathi eside, ukuhlanza okuhlukahlukene kubeka kalula kalula.
Emva kwalokhu, isiteleka esiphezulu senziwa, lapho isimo sesiguli sigula khona futhi sinciphise kancane. Ngalesi sigaba ekuthuthukiseni isifo sikaHirschsprung kubantu abadala, isisindo somzimba sesinciphisa, bayakhathazeka ngenxa yesisindo esiswini nokuphefumula. Kwezinye izimo, kuphawulwe ukuthi kune-anemia ejulile nezifo eziphathelene nokuxilonga umzimba.
Isigaba esilandelayo sesi sifo sivunyiwe. Iziguli azisasetshenziswa ngokuhlanza ama-laxatives ahlukahlukene. Usenomzwelo wesisu esiswini esingaphansi, kanti futhi ukuvimbela emathunjini ngokushesha kukhula.
Ukuxilongwa kwesifo sikaHirschsprung
Uma kwenzeka ukusola ngesifo sikaHirschsprung, ukuhlolwa kwe-rectal kwenziwa kuqala. Ngaphambi kwesifo, i-ampoule engenalutho ye-rectum itholakala esigulini. Izwi le-sphincter landa. Kulesi simo, kuyadingeka ukuba ufunde irejistra yonke yezinhlaka zesisu esiswini. Ngesifo sikaHirschsprung, izingodo zamakoloni zikhulisiwe futhi zihlanjululwe, ngezinye izikhathi zibona amazinga amanzi.
Isiguli sidinga futhi ukuba sibe nesigmoidoscopy, irrigography, colonoscopy kanye nokuxilongwa kwe-histochemical.
Ukwelashwa kwesifo sikaHirschsprung
Indlela kuphela yokuphatha isifo sikaHirschsprung ukuhlinzwa. Izinhloso eziyinhloko zokusebenza yilena:
- ukukhishwa kweminyango yonke;
- ukususwa kwendawo ye-aganglionic;
- ukulondolozwa kwengxenye yamathumbu amakhulu asebenzayo.
Ezinganeni, imisebenzi ka-Swanson's, iDuelel's kanye neSoave yama-radical iye yasungulwa. Abantu abadala ukusebenza kwabo ngendlela evamile kuyaphikisana ngenxa yezici zesifo nesifo esibucayi esibucayi emathunjini emisipha noma amancane emathumbu. Ngokuvamile, ngesifo sikaHirschsprung, ukusebenza kukaDuhamel kuguqulwa, lapho indawo ye-aganglionary isuswe khona lapho kudalwa isiqu esifushane se-rectum. Ezimweni eziningi, kungenzeka ukuvimbela umonakalo ku-sphincter we-anus bese udala i-anastomosis engafani.
Ngaphambi kokuhlinzwa, isiguli sidinga
Isibikezelo esiphelele sesifo sikaHirschsprung ngemuva kokuhlinzwa siyancipha. Kodwa kwezinye izimo, ukuhlinzwa okuphindaphindiwe kungadingeka. Cishe ngaso sonke isikhathi isisekelo sokusebenza okunjalo sincishisiwe kuze kube yilapho kuvuselelwa i-anastomosis futhi kwenziwa ngokusebenzisa i-peritoneal noma i-perineal access.