I-purpura ye-Thrombocytopenic - iyini ingozi yesifo?

Zonke izinhlobo zezifo zegazi (i-hemorrhagic) ziyinto evamile emithi yesimanje. Amacala angu-50% ayi-purpura ye-thrombocytopenic, izimbangela zazo ziningi futhi azifani. Lesi sifo sithinta umzimba nganoma yisiphi isikhathi.

I-purpura ye-Thrombocytopenic

Isifo se-Verlhof noma i-thrombocytopenic purpura, izimbangela zazo ezingaziwa kahle kuze kube manje-into eyenza isosayensi waseJalimane emuva ngo-1735. Kubantu kuthiwa "isifo sobala" ngoba ezigulini ezinjalo ebusweni bomzimba lapha nalapha zibonakala zihlaselwa ngamasayizi ahlukene.

Izifo, iningi lamacala, zenzeka ezinganeni kusukela ekuzalweni kuze kube sekukhuleni, bese ziphela ngokuphelele ngaphandle kwezinyathelo zokwelapha. Ezinganeni ezingaphansi kweminyaka emibili, amacala e-purpura avame ukurekhodwa kubafana. Lapho usukhulile, lokhu kutholakala kwenzelwa iziguli ezingu-1-13 ezivela kubantu abayizinkulungwane ezingu-100, kanti iningi lamacala abe ngabesifazane.

Amafomu we-thrombocytopenic purpura

Isifo segazi njenge-thrombocytopenic purpura (isifo sikaVerff) senzeke lapho amangqamuzana egazi - amaplatelet, ehlushwa amasosha omzimba awo futhi afe ngaphambi kwesikhathi. Inkathi yokuphila kwabo esikhundleni sezinsuku ezingu-7-10, amahora amaningana. Ukuze kusetshenziswe abahlukumezi abazimele, i-spleen inesibopho. Lesi sifo sinamafomu amaningana axhomeke esibangelwa yisifo, kodwa ahluke kancane embonweni yezinkinga:

Amafomu we-thrombocytopenic idiopathic purpura, kungakhathaliseki ukuthi izimbangela ziphi, zihlukaniswe ngokuthi:

Yenza ngokuzenzakalelayo i-purpura ye-thrombocytopenic

Kwezinye izimo, umzimba uqala ukusebenza ngokumelene nawo. Lokhu kuyinhlobonhlobo ye-autoimmune yesifo. Ama-platelets abhujiswa amasosha omzimba, awabona njengamaseli angaphandle. Lolu hlobo lwesifo ngezinye izikhathi luvela ngokumelene nesizinda senye inqubo ye-autoimmune emzimbeni. Idiopathic thrombocytopenic purpura ibonakala ngokubhujiswa kwamaplatelets ayo ngaphansi kwezinto eziningana. Ngezinye izikhathi lokhu kuyisifo sokudlulisa izakhi zofuzo, nakuba ezimweni eziningi izimbangela zesifo esenzekayo zilandelayo:

I-heteroimmune thrombocytopenic purpura

Lapho eseyingane, inguqulo ye-heteroimmune (okungewona omzimba) yalesi sifo yi-thrombocytopenic purpura ye-thrombotic, ivela kaningi kunabantu abadala. Izindaba ezinhle ukuthi ukuhlaziywa kwezingane zokuthola isimo kulungile. Izimbangela zesifo yizi:

I-purpura ye-Thrombocytopenic - izimpawu

Lesi sifo seVerlhof, izimpawu zazo ezivelele kakhulu, zihluke esikhathini sokubonakala kwesimiso semvula. Lokhu kungukuthi, ekuqaleni, izivunguvungu noma, njengoba zibizwa ngokufanele ngamagqirha - i-petechiae, zibonakaliswa ngokugqamile, kancane kancane zinciphisa ubukhulu bombala bese ziphenduka i-cyanotic, i-hue eluhlaza, kancane kancane ziphenduka ophuzi. Ngesinye isikhathi ngokuhamba kwesikhathi, zonke izinhlobo zemivimbo zingase zibe emzimbeni, okuyisithombe esesabekayo, kodwa akusizi ubuhlungu, ngokungafani nokulimala komsuka omubi kumuntu onempilo.

Izibhamu zitholakala ikakhulukazi emlenzeni, kancane kancane emzimbeni, futhi zingavamile ukubhekana nazo, kodwa ama-mucous ahlukile. I-purpura ye-Thrombocytopenic inezimpawu ezifanayo kubantu abahlukene. Zingase ziphakame ngenxa ye-microtrauma, futhi ngaphandle kwesizathu. Ngokuyisisekelo, isifo senhliziyo senzeke ebusuku. Kulesi simo, isiguli asizwa ubuhlungu, ngaphandle kwesifo se-cerebral, lapho isiguli sidinga ngokuphuthumayo esibhedlela. Ukuhlukanisa:

Ukuxilongwa kwe-thrombocytopenic purpura

I-Verlhof isifo, okutholakala ukuthi akupheli ngokutholakala kwezimpawu, kusekelwe emiphumeleni yocwaningo lwelabhoratri yeziguli kanye nokuhlolwa komtholampilo. Odokotela benza i-anamnesis lapho i-thrombocytopenic purpura ibonakala khona okokuqala. Ngemuva kokuba izifo ezithinta izifo zitholakale futhi izinhlobonhlobo zezifundo zenziwa ngokuthatha igazi ukuze zihlaziywe, ngaphambi kokuhlola ukuphuma kwegazi. Lokhu kufaka:

  1. Ukuhlolwa kwe-cuff, uma i-cuff yesilinganiso sokucindezelwa ihlanganiswa imizuzu engu-10. Uma ekugcineni kwalezi zikhathi zamachashazi ezigaqekayo ezakhiwe ngaphansi kwenkomishi, ukuhlolwa kulungile. Lenziwa ezinganeni ezivela eminyakeni emithathu ubudala.
  2. Ukuhlolwa kuhlanganiswa lapho kusetshenzwa i-tourniquet yezokwelapha engxenyeni, okwathi ngemva kwesikhashana inikeza ukulimaza - le ndlela ifanele iziguli ezindala.

I-purpura ye-Thrombocytopenic, ifaka uchungechunge lwezivivinyo ezizobonisa isithombe esithembekile segazi lesiguli. Lokhu kufaka phakathi ukuhlolwa kwegazi:

Ngaphezu kwalokho, ezimweni ezinzima noma ngokungathembeki kwezinye izinhlobo zokuxilongwa kwe-thrombocytopenic purpura, i-bone marrow biopsy yenziwa - trepanabiopsy. Ngosizo lwethini elikhethekile le-trepan, i-puncture encane yomgogodla eyenziwa esifundeni se-lumbar ukuthatha inani elincane lamathambo, i-periosteum kanye ne-cerebrospinal fluid yokuhlaziywa.

I-purpura ye-thrombocytopenic

Izifo zegazi zidinga isimo sengqondo esingathĂ­ sina, ngoba impilo yesiguli kunoma yikuphi ubudala ixhomeke kakhulu kulokhu. Ukwelashwa kwe-thrombocytopenic purpura kwenziwa kokubili esibhedlela (phakathi nesigaba sokukhushulwa) nasekhaya. Kuyisibopho sokunikeza isiguli ukuphumula okuphezulu nokulala kombhede ukuze unciphise inani lezikhathi ezibuhlungu. Ngalesi sizinda, izindlela zokwelapha zendabuko zisetshenziselwa ngokuhambisana nemithi yomuntu. Kubalulekile ukunamathela ekudleni okuthile.

Ukuphiliswa kwesifo sikaVerff?

Kuye ngokuthi yikuphi ubudala nokuthi yisiphi isigaba i-Verlhof isifo esitholiwe, kuyoba nombuzo wokuguqulwa kwayo. Ngesikhathi esemncane, ukubikezela ukuthi kulungile, uma ingane ithola ukuthi isheshe futhi iphumelele ukunqoba ezinyangeni eziyisithupha. Emva kwalesi sikhathi, ukuxilongwa kuyahlala kungapheli, futhi kuzwakala sengathi i-thrombocytopenia enamandla.

Abantu abadala banenhlanhla - le nkinga ingabahamba nayo yonke impilo yabo ngezikhathi zokuxolelwa nokukhushulwa. Kwezinye izimo, i-thrombocytopenic purpura engapheli ingaphiliswa lapho isundu sisusiwe, nakuba lokhu akuqinisekisi 100%. Lesi sitho sibhubhisa amaplatelets futhi yisitha somzimba. Le ndlela isetshenziselwa ukuphikisana kokugcina, lapho ezinye izinhlobo zokwelashwa zingasebenzi. Sebenzisa njengohlelo lwe-cavitary, futhi ngosizo lwe-laparoscopy.

I-purpura ye-Thrombocytopenic - izidakamizwa

Umgomo wendlela yokwelapha isifo seVerlhof ukugcina izinga lamaplatelets egazini elidingekayo. I-pediopathic thrombocytopenic purpura iphathwa, ezimweni eziningi ngokuphumelelayo, okuvumela ukuthi kutholakale ukukhululwa okuzinzile iminyaka eminingi. Uma ngabe ukwelashwa noma ukuhlinzwa akusizile, uhlelo lokuthatha imithi luguqulwa lube olusha. Ukuze wenze lokhu, sebenzisa:

  1. I-Prednisolone (i-Methylprednisolone) yisidakamizwa esine-hormone esine-steroid, ukunciphisa umsebenzi wokuzivikela. Isetshenziswa ezinyathelweni zokuqala zokwelapha, ngaphambi kokususwa kwesipere.
  2. I-Interferon a2 isetshenziselwa ukuvimbela ama-antibodies ayo, uma izidakamizwa ze-steroid zingenamandla.
  3. I-Immunoglobulin G isetshenziswe ngaphambi kokuhlinza ukwandisa izinga lamaplatelets.
  4. Ama-immunosuppressants (i-Cyclophosphamide, i-Vincristine ne-Azathioprine) isetshenziswa uma isiguli singaboni omunye ukwelashwa. Kukhona ukuvimbela ama-antibodies egazini, okuholela ekwandeni kwenani lamaplatelet.
  5. Isidakamizwa i-Danazol, eshukumisa i-pituitary gland nge-reception eside sithinta kahle isithombe segazi.

Purpura - Thrombocytopenic - ukwelashwa ngamakhambi abantu

I-thrombocytopenic purpura enamandla iyisifo segazi, ngakho-ke amalungiselelo okwelapha ama-herbal (decoctions) anezindawo ze-hemostatic asetshenziselwa ngempumelelo ukwelashwa kwayo:

Ukudla nge purpura ye-thrombocytopenic

Akukho ukudla okhethekile kokugula kukaVerlhof. Kubalulekile ukuthi izitsha zisetshenziswe ngendlela efudumele noma epholile. Imifino yemvelo ene-thrombocytopenic purpura, njengezithelo iyasiza kakhulu kodwa akufanele ibangele ukubola. Uhlu lwemikhiqizo enconyiwe lufaka:

Kubalulekile ukukhipha okuvela ekudleni:

I-purpura ye-Thrombocytopenic - izinkinga

Lesi sifo sikaVerlhof, obhekene nezinkinga eziyingozi kakhulu, sidinga ukuphathwa kwezempilo ngokuqinile. Izinkinga zihlanganisa:

I-purpura ye-thrombocytopenic - ukuvimbela

Uma isiguli sithola ukuthi sinesifo se-thrombocytopenic purpura, lokhu kusho ukuthi impilo yomuntu kufanele ilahle imikhuba eminingi, kokubili okulimazayo nokujwayelekile, ukuguqula indlela yokuphila. Izinyathelo ezivimbelayo zihloswe ukugcina izinga lamaplatelet ne-hemoglobin ngenxa yokudla okucebile, kanye nokungabikho kwezici ezinzima: