I-Hyperplasia yezingqungquthela ze-adrenal

I-Hyperplasia iqala ngenxa yokukhula kwamaseli. Ngakho-ke, hlukanisa phakathi kwezicubu ze-hyperplasia, i-epithelium, ne-mucosa. Lesi sifo singenzeka kunoma yimuphi umzimba womuntu. I-Hyperplasia ye-adrenal gland iqala ngokuqondile ngesikhathi sokungena kwe-intrauterine. Lona uhlobo lokuzalwa lwesifo, okuvame ukuchazwa ngokuphazamiseka kokusebenza komzimba wesifazane okhulelwe, kanye ne-toxemia eqinile. Kunezinye izizathu eziningi ukuthi i-hyperplasia ye-grenal adrenal ihlotshaniswa nayo.

I-hyperplasia yezinhlayiya ze-adrenal - izimpawu

Lesi sifo senziwa abesifazane kakhulu kaningi kunamadoda. Ezimweni eziningi, kukhona amafomu akhiphekile okunzima ukuwabona lapho kungekho khona izimpawu ezicacile. I-hyperplasia ye-cortex adrenal ivame ukutholakala eminyakeni yokuqala yokuphila kwengane. Kukhona amacala uma inqubo enjalo isenziwa lapho umuntu ekhulile, bese kubonakala ukutholakala kwempilo.

Izimpawu, ngokuvamile, zixhomeke esimweni senkambo yesifo. Njengomthetho, i-adrenal hyperplasia yisifo sokubeletha, uhlobo oluthile olutholakalayo aluvamile. Singakwazi ukuhlukanisa ezinye zezibonakaliso ezibonisa ukuba khona kwalesi sifo:

I-hyperplasia yama-congenital ye-cortex ye-adrenal - ukwelashwa

Njengoba ifomu lokubeletha livame kakhulu, cabanga izindlela zokuphatha lolu hlobo lwesifo. I-Hyperplasia ye-grenal adrenal ibonakala ukwehla komsebenzi wezinye ze-enzyme ezihilela ngokuqondile ku-biosynthesis ye-cortisol. Ukukhubazeka okunjalo kungokwemvelo, ngaleyo ndlela bezibonakalisa kuphela kubantwana abasha. Kubantu abadala, izimpawu zingase zibe ezingeni elihlukile, okuvame ukuholela ekudidekeni phakathi kodokotela.

Ukwelashwa kwalesi sifo kuncike kuhlelo, olwenziwe ngomuntu ngamunye. I-hyperplasia ayikwazi ukuphulukiswa ngamakhambi abantu noma ekhaya, njengoba ukwelashwa okuyinkimbinkimbi kudinga ukuphathwa okuqinile kwezokwelapha nokuhlolwa okuqhubekayo. Njengomthetho, izidakamizwa ezikhethekile zenzelwe ukunciphisa ukukhiqizwa kwe-ACTH. Kungaba i-Prednisolone noma i-Cortisone emazingeni aphezulu kakhulu ngesonto lokuqala lokulashwa. Ngemva kwalokho, umthamo wehlisiwe, kancane kancane ukunciphisa ukungenisa okungenani, ukulawula ukukhiqizwa kwe-ACTH yokukhiqiza. Lokhu kusekelwa kubafana kwenziwa ngaphambi kokukhulelwa, nakumantombazane kulo lonke impilo yabo. Abesifazane kufanele baphenye njalo futhi bathathe imithi efanelekile. Ngokuvamile, amantombazane aneziphambeko ezinzima ezithombeni zofuzo enza ukuhlinzwa kweplastiki. Kulokho konke, ukwelashwa okungeziwe kunqunywe njengokusungulwa kwesisombululo somzimba esiqukethe i-5% i-glucose no-1-2 mg ngekhilogremu yesisindo se-doxa. Lapho esekhulile, abesifazane abakunconywa ukuba bahlele ukukhulelwa kwabo, futhi kwezinye izimo ukuzala. Ngakho-ke, ukuxilongwa ngabanye kuphela kunganikeza impendulo ekukhuleni kwengane nokubeletha.

Singasho ukuthi indlela eyinhloko yokwelapha i-hyperplasia lapho umuntu esemdala ukususwa ngokuphelele kwezinso nazo zonke izingxenye zalo, uma kungeyona umzimba womntwana.