I-Hemochromatosis yesibindi isifo sofuzo esivela ekugqeni kwensimbi emzimbeni. Uma ukushintshaniswa kwensimbi kuphazamiseka, ukuqoqwa kwalo kuyenzeka, futhi lokhu kubangela izimpawu eziningi zobuningi.
I-Hemochromatosis ivela ekuguquleni kwezakhi zofuzo, okubangela ukuthi umzimba uthathe insimbi eningi kakhulu, efaka isibindi, inhliziyo kanye ne-pancre nezinye izitho. Kubonakala, njengomthetho, emadodeni eminyakeni engu-40-60, nakwabesifazane ekudala.
Izimpawu ze-hemahromatosis
Ezokwelapha, kunezinhlobo ezimbili ze-hemochromatosis:
- i-hemochromatosis eyinhloko yilokho okuthiwa i-hemochromatosis yefa, okuvela njengesifo se-innate; libhekene nomthunzi wethusi okwakusesikhumba, zonke izindawo ngaphandle kwamapendeni, kanye nobuthakathaka, ukunganaki, ukukhathala, ukucindezeleka kwegazi okuphansi, ukulahlekelwa izinwele , ubuhlungu obuhlangene nokulahlekelwa isisindo;
- i-hemochromatosis yesibili - lokhu kungenxa yomphumela oyinhloko, noma umphumela wokudla okungalawulwa kwezidakamizwa ngensimbi; ngezinye izikhathi kungavela ngenxa yezifo ezithile zesibindi negazi.
Nge-hemochromatosis, isiguli siba nesifo se-cirrhosis, futhi kwezinye izimo umdlavuza wesibindi.
Uma ama-pancreas ethinteka, isifo sikashukela singenzeka.
Uma ubuchopho buyathinteka, insimbi ifakwa emgodini we-pituitary futhi ibangele ukuphazamiseka ohlelweni lwe-endocrine, oluthinta kakhulu imisebenzi yezocansi.
Ukulimala kwenhliziyo kuphazamisa isigqi senhliziyo, futhi ku-20-30% ukuhluleka kwenhliziyo kungabonakala.
Umthelela owonakalayo wensimbi ngokweqile emzimbeni uholela ezifweni ezithathelwanayo njalo.
Ukuxilongwa kwe-hemochromatosis
Nale nkinga udinga uxhumane ne-gastroenterologist. Ukuze kutholakale ukuxilongwa, ngaphezu kokuhlolwa kukadokotela nokucaciswa kwezimpawu, ukuhlolwa kwegazi kanye nokuhlolwa kwegazi jikelele.
Uma kukhona amacala afanayo emlandweni womndeni, lokhu nakho kuyinkomba ebalulekile ekuxilongweni. Iqiniso liwukuthi ngaphambi kokubonakaliswa kwangaphandle kwe-hemochromatosis kunesikhathi esiningi kusukela izindinganiso zensimbi ziphuma esikalini.
Okunye ukuhlolwa okubalulekile - i-ultrasound, enquma isimo sesibindi nezinye izitho zomuthi wamathumbu. Ngezinye izikhathi i-MRI iyadingeka. Ezinye izinhlobo zokuhlolwa azihlinzeki ngemininingwane ethile ngesifo, futhi zisiza kuphela ukuqapha isimo sezinye izitho nezinhlelo. Ngakho-ke, kulokho okunye, ukuhlolwa kuxhomeke ezimpawu kanye nokuqina kwesifo.